CHR 2018

DATA SUMMARIES

The summaries below were produced from the Canadian Blood Disorders Registry, which covers all of Canada except for British Columbia. Data was added for British Columbia where available. As the 2018 numbers were the first produced from CBDR instead of the CHR registry, there may be reductions or increases in the numbers of patients diagnosed. Further reports for additional rare blood disorders previously covered by CHR reporting will be added by the end of August, 2019. Future reports will be produced from CBDR.

This data was compiled based on information in CBDR as of the end of 2018.

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INDIVIDUALS WITH FACTOR VIII DEFICIENCY

1. FVIII stats can 2018
'Hemophilia A' grouped by:

A. Severity (Severe ≤1%, Moderate = 1-5%, Mild ≥ 5%); and

B. Age, according to Statistics Canada age groups; and

C. Gender (females can be registered if factor levels are ≤40%).

2. FVIII ped adult 2018
Same as 1, but age grouped according to pediatric (<18 years) & adult (≥18 years ).

INDIVIDUALS WITH FACTOR IX DEFICIENCY

3. FIX stats can 2018
'Hemophilia B' grouped as for those with factor VIII deficiency.

4. FIX ped adult 2018
Same as 3, but age grouped according to pediatric (<18 years) & adult (≥18 years ).

INDIVIDUALS WITH VON WILLEBRAND FACTOR DEFICIENCY

5. VWD stats can 2018
Grouped by age and by type.

6. VWD ped adult 2018
Same as 5, but age grouped according to pediatric (<18 years) & adult (≥18 years ).

RARE INHERITED COAGULATION DISORDERS

To be added

RARE INHERITED PLATELET DISORDERS

To be added

INDIVIDUALS WITH C1 ESTERASE INHIBITOR DEFICIENCY

7. c1 Esterase stats can 2018
Grouped by age and gender

INDIVIDUALS WITH CONGENITAL HYPOGAMMAGLOBULINEMIA

8. Hypogammaglobulinemia stats can 2018
Grouped by age and gender